The general structure of phosphatidylglycerol consists of a L-glycerol 3-phosphate backbone ester-bonded to either saturated or unsaturated fatty acids on carbons 1 and 2. The head group substituent glycerol is bonded through a phosphomonoester. It is the precursor of surfactant and its presence (>0.3) in the amniotic fluid of the newborn indicates fetal lung maturity.
Approximately 98% of alveolar wall surface area is due to the presence of type I cells, with type II cells producing pulmonary surfactant covering around 2% of the alveolar walls. Once surfactant is secreted by the type II cells, it must be spread over the remaining type I cellular surface area. Phosphatidylglycerol is thought to be important in spreading of surfactant over the Type I cellular surface area. The major surfactant deficiency in premature infants relates to the lack of phosphatidylglycerol, even though it comprises less than 5% of pulmonary surfactant phospholipids. It is synthesized by head group exchange of a phosphatidylcholine enriched phospholipid using the enzyme phospholipase D.
Biosynthesis
Phosphatidylglycerol (PG) is formed via a complex sequential pathway whereby phosphatidic acid (PA) is first converted to CDP-diacylglyceride by the enzyme CDP-diacylglyceride synthase.[2] Then a PGP synthase enzyme exchanges glycerol-3-phosphate (G3P) for cytidine monophosphase (CMP), forming the temporary intermediate phosphatidylglycerolphosphate (PGP).[3] PG is finally synthesized when a PGP phosphatase enzyme catalyzes the immediate dephosphorylation of the PGP intermediate to form PG.[4] In bacteria, another membrane phospholipid known as cardiolipin can be synthesized by condensing two molecules of phosphatidylglycerol; a reaction catalyzed by the enzyme cardiolipin-synthase.[5] In eukaryotic mitochondria phosphatidylglycerol is converted to cardiolipin by reacting with a molecule of cytidine diphosphate diglyceride in a reaction catalyzed by cardiolipin synthase.[6]
^Richard J. King; Mary Catherine MacBeth (6 October 1981). "Interaction of the lipid and protein components of pulmonarysurfactant Role of phosphatidylglycerol and calcium". Biochimica et Biophysica Acta (BBA) - Biomembranes. 647 (2): 159–168. doi:10.1016/0005-2736(81)90242-X. PMID6895322.
^Hostetler KY, van den Bosch H, van Deenen LL (March 1972). "The mechanism of cardiolipin biosynthesis in liver mitochondria". Biochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism. 260 (3): 507–13. doi:10.1016/0005-2760(72)90065-3. hdl:1874/17621. PMID4556770. S2CID46101728.
Hostetler KY, van den Bosch H, van Deenen LL. The mechanism of cardiolipin biosynthesis in liver mitochondria. Biochim Biophys Acta. 1972 Mar 23;260(3):507-13. doi:10.1016/0005-2760(72)90065-3. PMID 4556770.