Non-cirrhotic portal fibrosis
Non-cirrhotic portal fibrosis is inherited in an autosomal recessive manner

Non-cirrhotic portal fibrosis (NCPF) is a chronic liver disease^[1] and type of non-cirrhotic portal hypertension (NCPH).

It is characterized by 'obliterative portovenopathy', which leads to various problems such as portal hypertension, massive splenomegaly, and variceal bleeding. It is estimated that about 85% of people with NCPF have repeated episodes of variceal bleeding.^[2]

Hallmark of the disease is thrombosis/sclerosis of branches of portal vein. Vessels formed are often termed as mesangiosinusoids or periportal cavernoma.^{[citation needed]}

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