Salivary gland atresia is congenital blockage or absence of the orifice of a major salivary gland duct or part of the duct itself.[1]
It is a very rare condition.[1][2] The submandibular salivary gland duct is usually involved, having failed to cannulate during embryological development. The condition first becomes apparent in the first few days after birth where a submandibular swelling caused by a retention cyst is noticed.[2]